Turcot's syndrome
A case report
Keywords:
Turcot’s Syndrome, Tubulovillous adenoma, AstrocytomaAbstract
The case of a 15 year old patient with Turcot’s syndrome is described. The patient had a mass that protruded from the rectum, which was diagnosed as tubulovillous adenoma; simultaneously she was diagnosed with anaplastic as- trocytoma Grade 3, a brain mass. Her family medical history shows that some family members have submitted in colon cancer. All these data suggest that patient had type 2 Turcot syndrome, a rare disorder in hospital consultation. The diagnosis and treatment of the patient required multidisciplinary action, the rarity of this disorder hinders the proper diagnosis of it, and so anatomicpathology studies of cases where the simultaneous formation of tumor pro- cesses, in colon and SNC, should be an indication for specialist.
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