Kartagener Syndrome
Case report
Keywords:
Kartagener syndrome, dextrocardia, primary ciliary dyskinesiaAbstract
Kartagener syndrome is an autosomic recessive hereditary disease characterized of primary ciliary dyskinesia, chro- nic cough, chronic sinusitis, infertility, situs inversus, and bronchiectasis. We report the case of a patient male of 36 years old and history of dextrocardia, who consulted of recurrent respi- ratory symptoms whit inadequate response to previous treatments, with beta-adrenergic and oral antibiotics since childhood. was referred to an outpatient service Pneumology and Cardiology Hospital ESE-CARI, high complexity, where chest radiograph posteroanterior is performed, showing dextrocardia plus pneumatocele and possible infectious process. A history of infertility, recurrent episodes pansinusitis, lower respiratory symptoms and imaging findings, aroused the suspicion of primary ciliary dyskinesia like a Kartagener syndrome. Our purpose in presenting this case, is that we think that, although it is an extremely rare disease, represents a possible diagnosis when hemoptysis and history of infertility are associated.
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References
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