Pancreatic acquired hemochromatosis
Keywords:
Hemochromatosis, Iron metabolism disorders, Ferritins, TransferrinAbstract
In this article we present the case of a female patient aged 39 years olds, with a history of refractory anemia and chronic kidney disease who consulted the emergency department for acute chronic abdominal pain associated with vomiting, loose stools and fever; pancreatic enzyme elevation was noted in paraclinical; was admitted to the Intensive Care Unit (ICU) of a university hospital in Barranquilla (Colombia), with diagnostic impression of acute pancreatitis, which was discarded later. The history of multiple blood transfusions and clinical-chemical correlation led to the diagnosis of pancreatic acquired hemochromatosis; whose presentation is a rare variant in disease. Because of the impossibility of pancreatic biopsy, diagnostic confirmation was performed by nuclear magnetic resonance and serum ferritin and transferrin saturation. The patient was treated with iron chelators and erythropoietin obtaining clinical improvement.
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